A case of hereditary angioedema: special reference to perioperative management
نویسندگان
چکیده
منابع مشابه
Perioperative management for patients with hereditary angioedema
Hereditary angioedema (HAE) is a rare autosomal dominant disease that results from mutations in the C1-esterase inhibitor (C1-INH) gene. HAE is characterized by recurrent episodes of angioedema of the skin (face, extremities, genitalia, trunk), the gastrointestinal tract, and respiratory tract. Symptoms experienced can be debilitating, may impact quality of life, and can be life threatening. Pr...
متن کاملAngioedema: Perioperative management
OBJECTIVE To describe the perioperative management of a patient with acquired angioedema (AAE). METHODS A 66-year-old Caucasian male presented from an outside hospital with a history of acquired angioedema and gastrointestinal stromal tumor-related intractable urticaria and mastocytosis. He was admitted for urgent laparoscopic partial gastrectomy, secondary to gastric outlet obstruction sympt...
متن کاملPerioperative care of a patient with hereditary angioedema
Hereditary angioedema is a rare disorder caused by the congenital deficiency or dysfunction of C1 inhibitor. The deficiency results in recurrent episodes of angioedema, mainly involving the mucosa and skin. The most common clinical manifestations are the result of edema in the subcutaneous tissue, abdominal mucosa, and laryngeal tissue. Laryngeal involvement remains the most serious due to the ...
متن کاملPerioperative Management of a Patient with Hereditary Angioedema (HAE) Undergoing Endometrial Ablation: A Case Report and Review of Literature
MOJ Womens Health 2017, 5(4): 00129 Perioperative prophylaxis with Danazol and C1 inhibitor concentrate (C1-INH) are commonly used to prevent angioedema episodes. Anaesthesia management and perioperative implications have been recently commented by some authors [3]. Airway oedema and hypovolemic shock due to the tissue leak of fluids are especially significant in the perioperative period, chall...
متن کاملPerioperative Management of a Patient with Hereditary Angioedema undergoing Lumbar Interbody Arthrodesis
Hereditary angioedema (HAE) is a rare genetic disorder resulting from an inherited deficiency or dysfunction of the C1-esterase inhibitor. It is characterized by recurrent and self-limiting angioedema episodes, most often affecting the skin or the mucosal tissues of the upper respiratory and gastrointestinal tracts. Androgens and fresh frozen plasma (FFP) are frequently used as treatment despit...
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ژورنال
عنوان ژورنال: Japanese Journal of Oral & Maxillofacial Surgery
سال: 2005
ISSN: 2186-1579,0021-5163
DOI: 10.5794/jjoms.51.260